Nevus Flammeus in Tuberous Sclerosis
نویسندگان
چکیده
Hypoalbuminemia in the absence of hepatic, renal, and nutritional deficiency may indicate protein malabsorption or protein losing gastroenteropathy. Abuse of laxatives like castor oil can cause protein losing gastroenteropathy(l). Castor oil is hydrolyzed in the intestine by pancreatic lipase to glycerol and ricinoleic acid. Ricinoleic acid acts as a mild irritant and causes purgation. It is also known to interfere with absorption of proteins, resulting in protein losing enteropathy(2).
منابع مشابه
The case of a boy with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita: a unique instance of phacomatosis pigmentovascularis*
Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed vari...
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Phacomatosis Pigmentovascularis is a rare syndrome characterized by capillary malformation and pigmentary nevus. A case of a 2-year-old patient is reported, who presented extensive nevus flammeus and an aberrant Mongolian spot, without systemic disease, manifestations that allow us to classify this case as type IIa Phacomatosis Pigmentovascularis, according to Hasegawa's classification.
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cutaneous vascular and pigmentary lesions. The pregnancy of his mother and family history were unremarkable. Physical examination showed bilateral nevus flammeus involving the scalp, face, neck, trunk, upper part of the back, scrotum and the flexor sides of arms and thighs. Large, bluish-grey pigmentation was observed on the abdominal area, back, buttocks, legs and the extensor sides of the arm...
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The association of a vascular lesion with melanocytic nevi was first described by Ota et, al in 1947, and given the name phakomatosis pigmentovascularis(PPV). Later on this term was used for the cases with simultaneous occurrence of congenital vascular and pigmented (epidermal or melanocytic) anomalies. Our first case is a 12-year-old Kuwaiti boy who had extensive port-wine stain (nevus flammeu...
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638 Ann Dermatol Received April 5, 2016, Revised September 7, 2016, Accepted for publication September 9, 2016 Corresponding author: Sang Seok Kim, Department of Dermatology, Kangdong Sacred Heart Hospital, Hallym University College of Medicine, 150 Seongan-ro, Gangdong-gu, Seoul 05355, Korea. Tel: 82-2-2224-2285, Fax: 82-2-474-7918, E-mail: [email protected] This is an Open Access article dist...
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